| Item type |
学術雑誌論文 / Journal Article(1) |
| 公開日 |
2013-09-24 |
| タイトル |
|
|
タイトル |
出生時より巨大な血管腫を持つカサバッハ・メリット症候群の新生児2例 : 大きく異なった治療反応性 |
|
言語 |
ja |
| タイトル |
|
|
タイトル |
Two Newborn Casese of Kasabach-Merritt Syndrome with Large Congenital Hemangiomas at Birth |
|
言語 |
en |
| 言語 |
|
|
言語 |
jpn |
| 主題 |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
congenital hemangioma |
| 主題 |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
Kasabach-Merritt syndrome |
| 主題 |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
prednisolene |
| 主題 |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
propranolol |
| 主題 |
|
|
言語 |
en |
|
主題Scheme |
Other |
|
主題 |
chemotherapy |
| 資源タイプ |
|
|
資源タイプ識別子 |
http://purl.org/coar/resource_type/c_6501 |
|
資源タイプ |
journal article |
| アクセス権 |
|
|
アクセス権 |
open access |
|
アクセス権URI |
http://purl.org/coar/access_right/c_abf2 |
| 作成者 |
矢野, 道広
蛇口, 美和
平井, 大士
深谷, 博志
久保田, 弘樹
近野, 勇樹
山田, 俊介
高橋, 勉
Yano, Michihiro
Hebiguchi, Miwa
Hirai, Daishi
Fukaya, Hiroshi
Kubota, Hiroki
Konno, Yuki
Yamada, Shunsuke
Takahashi, Tsutomu
|
| 内容記述 |
|
|
内容記述タイプ |
Abstract |
|
内容記述 |
Kasabach-Merritt syndrome （KMS） is a consumptive coagulopathy associated with the presence of large hemangiomas. KMS has a high mortality rate of nearly 30% due to the development of serious bleeding tendencies, high output heart failure caused by arteriovenous shunt flow and respiratory failure caused by direct compression by large hemangiomas. Although several treatments are administered to treat KMS patients, including steroids, interferon, anti-neoplasm agents, propranolol and radiation therapy, there are no recommended management strategies, except for the use of steroid therapy as first-line therapy. We herein report two newborn cases of KMS with large congenital hemangiomas at birth. Although the laboratory findings of these cases were very similar, their clinical courses were significantly different. In one case, in spite of having introduced various treatments, it took more than one year for the laboratory findings to improve and stabilize. However, in the other case, all laboratory findings normalized within three weeks after administering prednisolone only. We do not know why this disparity occurred. It is important to clarify the histopathological differences between apparently similar vascular tumors. |
|
言語 |
en |
| 出版タイプ |
|
|
出版タイプ |
VoR |
|
出版タイプResource |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
| 書誌情報 |
ja : 秋田医学
巻 40,
号 1,
p. 23-28,
発行日 2013-06-28
|
| 収録物識別子 |
|
|
収録物識別子タイプ |
ISSN |
|
収録物識別子 |
03866106 |
| 収録物識別子 |
|
|
収録物識別子タイプ |
NCID |
|
収録物識別子 |
AN00009294 |
| 出版者 |
|
|
出版者 |
秋田医学会 |
|
言語 |
ja |
akitai40(23).pdf (1.4 MB)
