{"created":"2023-07-25T10:22:39.721511+00:00","id":2094,"links":{},"metadata":{"_buckets":{"deposit":"637338e6-8efd-4250-b57c-dbf20c7e2865"},"_deposit":{"created_by":3,"id":"2094","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"2094"},"status":"published"},"_oai":{"id":"oai:air.repo.nii.ac.jp:00002094","sets":["611:862:863:963"]},"author_link":["7913","7915","7918","7923","7922","7928","7921","7914","7924","7925","7927","7919","7916","7917","7920","7926"],"item_10001_alternative_title_1":{"attribute_name":"別タイトル","attribute_value_mlt":[{"subitem_alternative_title":"Two Newborn Casese of Kasabach-Merritt Syndrome with Large Congenital Hemangiomas at Birth"}]},"item_10001_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2013-06-28","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"28","bibliographicPageStart":"23","bibliographicVolumeNumber":"40","bibliographic_titles":[{"bibliographic_title":"秋田医学"}]}]},"item_10001_description_5":{"attribute_name":"内容記述（抄録）","attribute_value_mlt":[{"subitem_description":"Kasabach-Merritt syndrome （KMS） is a consumptive coagulopathy associated with the presence of large hemangiomas. KMS has a high mortality rate of nearly 30% due to the development of serious bleeding tendencies, high output heart failure caused by arteriovenous shunt flow and respiratory failure caused by direct compression by large hemangiomas. Although several treatments are administered to treat KMS patients, including steroids, interferon, anti-neoplasm agents, propranolol and radiation therapy, there are no recommended management strategies, except for the use of steroid therapy as first-line therapy. We herein report two newborn cases of KMS with large congenital hemangiomas at birth. Although the laboratory findings of these cases were very similar, their clinical courses were significantly different. In one case, in spite of having introduced various treatments, it took more than one year for the laboratory findings to improve and stabilize.　However, in the other case, all laboratory findings normalized within three weeks after administering prednisolone only. We do not know why this disparity occurred. It is important to clarify the histopathological differences between apparently similar vascular tumors.","subitem_description_type":"Other"}]},"item_10001_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"秋田医学会"}]},"item_10001_source_id_11":{"attribute_name":"NCID","attribute_value_mlt":[{"subitem_source_identifier":"AN00009294","subitem_source_identifier_type":"NCID"}]},"item_10001_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"03866106","subitem_source_identifier_type":"ISSN"}]},"item_10001_version_type_20":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"矢野, 道広"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"蛇口, 美和"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"平井, 大士"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"深谷, 博志"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"久保田, 弘樹"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"近野, 勇樹"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"山田, 俊介"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"高橋, 勉"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Yano, Michihiro","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Hebiguchi, Miwa","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Hirai, Daishi","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Fukaya, Hiroshi","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kubota, Hiroki","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Konno, Yuki","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Yamada, Shunsuke","creatorNameLang":"en"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Takahashi, Tsutomu","creatorNameLang":"en"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2017-02-16"}],"displaytype":"detail","filename":"akitai40(23).pdf","filesize":[{"value":"1.4 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"akitai40(23).pdf","url":"https://air.repo.nii.ac.jp/record/2094/files/akitai40(23).pdf"},"version_id":"ff9d68a8-d8bf-4a07-84f0-56ad73c5f4a9"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"congenital hemangioma","subitem_subject_scheme":"Other"},{"subitem_subject":"Kasabach-Merritt syndrome","subitem_subject_scheme":"Other"},{"subitem_subject":"prednisolene","subitem_subject_scheme":"Other"},{"subitem_subject":"propranolol","subitem_subject_scheme":"Other"},{"subitem_subject":"chemotherapy","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"出生時より巨大な血管腫を持つカサバッハ・メリット症候群の新生児2例 : 大きく異なった治療反応性","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"出生時より巨大な血管腫を持つカサバッハ・メリット症候群の新生児2例 : 大きく異なった治療反応性"}]},"item_type_id":"10001","owner":"3","path":["963"],"pubdate":{"attribute_name":"公開日","attribute_value":"2013-09-24"},"publish_date":"2013-09-24","publish_status":"0","recid":"2094","relation_version_is_last":true,"title":["出生時より巨大な血管腫を持つカサバッハ・メリット症候群の新生児2例 : 大きく異なった治療反応性"],"weko_creator_id":"3","weko_shared_id":-1},"updated":"2023-07-25T11:43:42.101535+00:00"}